Airway stenting in a child with spondyloepiphyseal dysplasia congenita: 13-year survival
01 Pubblicazione su rivista
Nenna Raffaella, Midulla Fabio, Masi Laura, Bacci Giacomo Maria, Frassanito Antonella, Baggi Roberto, Brandi Maria Luisa, Avenali Stefano, Mirabile Lorenzo, Serio Paola
ISSN: 0165-5876
We describe the case of a boy with spondyloepiphyseal dysplasia congenita. At birth, he experienced severe respiratory distress necessitating tracheotomy. Endoscopy done because mechanical ventilation failed to resolve desaturations disclosed severe tracheo-bronchomalacia. A Polyflex silicone stent was placed in the trachea (replaced by Y-Dumon stent) and 2 Palmaz metallic stents in the mainstem bronchi (overlapped with 2 Jomed stents 5 years later). Airway stenting guaranteed a suitable respiratory status and allowed a child who was expected to die at birth, to reach 13.5 years old in good conditions.