Pubblicazioni

On the complexities of measuring exercise âventilatory efficiencyâ in obstructive lung diseases

2019 - PEDIATRIC PULMONOLOGY

Neder, J. A.; Di Paolo, M.; O'Donnell, D. E.; Palange, P.

Biomarkers in pediatric lung diseases including cystic fibrosis

2019 - CURRENT RESPIRATORY MEDICINE REVIEWS

Parisi, G. F.; Papale, M.; Tardino, L.; Nenna, R.; Midulla, F.; Leonardi, S.

Assembly and functional analysis of an S/MAR based episome with the cystic fibrosis transmembrane conductance regulator gene

2018 - INTERNATIONAL JOURNAL OF MOLECULAR SCIENCES

De Rocco, Davide; Pompili, Barbara; Castellani, Stefano; Morini, Elena; Cavinato, Luca; Cimino, Giuseppe; MariggiÃ², Maria A.; Guarnieri, Simone; Conese, Massimo; Porto, Paola Del; Ascenzioni, Fiorentina

CFTR genotype and aerobic exercise capacity in cystic fibrosis. A cross-sectional study

2018 - ANNALS OF THE AMERICAN THORACIC SOCIETY

Radtke, Thomas; Hebestreit, Helge; Gallati, Sabina; Schneiderman, Jane E.; Braun, Julia; Stevens, Daniel; Hulzebos, Erik H. J.; Takken, Tim; Boas, Steven R.; Urquhart, Don S.; Lands, Larry C.; Tejero, Sergio; Sovtic, Aleksandar; Dwyer, Tiffany; Petrovic, Milos; Harris, Ryan A.; Karila, Chantal; Savi, Daniela; Usemann, Jakob; Mei-Zahav, Meir; Hatziagorou, Elpis; Ratjen, Felix; Kriemler, Susi; Study Group, CFTR-Exercise

Is daily physical activity affected by dynamic hyperinflation in adults with cystic fibrosis?

2018 - BMC PULMONARY MEDICINE

Savi, Daniela; Di Paolo, Marcello; Simmonds, Nicholas J.; Pascucci, Chiara; Quattrucci, Serena; Palange, Paolo

Exhaled markers of antioxidant activity and oxidative stress in stable cystic fibrosis patients with moderate lung disease

2018 - JOURNAL OF BREATH RESEARCH

Spicuzza, Lucia; Parisi, Giuseppe Fabio; Tardino, Lucia; Ciancio, Nicola; Nenna, Raffaella; Midulla, Fabio; Leonardi, Salvatore

Esculentin-1 aderived antipseudomonal peptides. limited induction of resistance and synergy with aztreonam

2018 - PROTEIN & PEPTIDE LETTERS

Casciaro, Bruno; Loffredo, Maria Rosa; Luca, Vincenzo; Verrusio, Walter; Cacciafesta, Mauro; Mangoni, Maria Luisa

Gut microbiota signatures in cystic fibrosis. Loss of host CFTR function drives the microbiota enterophenotype

2018 - PLOS ONE

Vernocchi, P.; Chierico, F. D.; Russo, A.; Majo, F.; Rossitto, M.; Valerio, M.; Casadei, L.; Storia, A. L.; De Filippis, F.; Rizzo, C.; Manetti, C.; Paci, P.; Ercolini, D.; Marini, F.; Fiscarelli, E. V.; Dallapiccola, B.; Lucidi, V.; Miccheli, A.; Putignani, L.

Clinical expression of cystic fibrosis in a large cohort of Italian siblings

2018 - BMC PULMONARY MEDICINE

Terlizzi, V.; Lucarelli, M.; Salvatore, D.; Angioni, A.; Bisogno, A.; Braggion, C.; Buzzetti, R.; Carnovale, V.; Casciaro, R.; Castaldo, G.; Cirilli, N.; Collura, M.; Colombo, C.; Di Lullo, A. M.; Elce, A.; Lucidi, V.; Madarena, E.; Padoan, R.; Quattrucci, S.; Raia, V.; Seia, M.; Termini, L.; Zarrilli, F.

22q and two: 22q11.2 deletion syndrome and coexisting conditions

2018 - AMERICAN JOURNAL OF MEDICAL GENETICS. PART A

Cohen, J. L.; Crowley, T. B.; Mcginn, D. E.; Mcdougall, C.; Unolt, M.; Lambert, M. P.; Emanuel, B. S.; Zackai, E. H.; McDonald-McGinn, D. M.

TG2 regulates the heat-shock response by the post-translational modification of HSF1

2018 - EMBO REPORTS

Rossin, F.; Villella, V. R.; D'Eletto, M.; Farrace, M. G.; Esposito, S.; Ferrari, E.; Monzani, R.; Occhigrossi, L.; Pagliarini, V.; Sette, C.; Cozza, G.; Barlev, N. A.; Falasca, L.; Fimia, G. M.; Kroemer, G.; Raia, V.; Maiuri, L.; Piacentini, M.

Aerosolized bovine lactoferrin reduces neutrophils and pro-inflammatory cytokines in mouse models of Pseudomonas aeruginosa lung infections

2017 - BIOCHEMISTRY AND CELL BIOLOGY

Valenti, Piera; Frioni, Alessandra; Rossi, Alice; Ranucci, Serena; De Fino, Ida; Cutone, Antimo; Rosa, Luigi; Bragonzi, Alessandra; Berlutti, Francesca

Six-minute walk test vs cardiopulmonary exercise test in the assessment of exercise tolerance in adults with cystic fibrosis

2017 - European Respiratory Journal

Di Paolo, Marcello; Savi, Daniela; Quattrucci, Serena; Graziano, Luigi; Arcieri, Elisabetta; Palange, Paolo

Severe disease in Cystic Fibrosis and fecal calprotectin levels

2017 - IMMUNOBIOLOGY

Parisi, Giuseppe Fabio; Papale, Maria; Rotolo, Novella; Aloisio, Donatella; Tardino, Lucia; Scuderi, Maria Grazia; Di Benedetto, Vincenzo; Nenna, Raffaella; Midulla, Fabio; Leonardi, Salvatore

A commentary on the novel complex allele [A238V; F508del] of the CFTR gene: clinical phenotype and possible implications for cystic fibrosis etiological therapies (INVITED)

2016 - JOURNAL OF HUMAN GENETICS

Lucarelli, Marco

Clinical expression of patients with the D1152H CFTR mutation

2015 - JOURNAL OF CYSTIC FIBROSIS

V., Terlizzi; V., Carnovale; G., Castaldo; C., Castellani; N., Cirilli; C., Colombo; F., Corti; F., Cresta; A., D'Adda; Lucarelli, Marco; V., Lucidi; A., Macchiaroli; E., Madarena; R., Padoan; Quattrucci, Serena; D., Salvatore; F., Zarrilli; V., Raia

Toward Repositioning Niclosamide for Antivirulence Therapy of Pseudomonas aeruginosa Lung Infections: Development of Inhalable Formulations through Nanosuspension Technology

2015 - MOLECULAR PHARMACEUTICS

Costabile, Gabriella; D'Angelo, Ivana; Rampioni, Giordano; BondÃ¬, Roslen; Pompili, Barbara; Ascenzioni, Fiorentina; Mitidieri, Emma; D'Emmanuele Di Villa Bianca, Roberta; Sorrentino, Raffaella; Miro, Agnese; Quaglia, Fabiana; Imperi, Francesco; Leoni, Livia; Ungaro, Francesca

Fighting microbial infections: A lesson from amphibian skin-derived esculentin-1 peptides

2015 - PEPTIDES

Luca, Vincenzo; Mangoni, Maria Luisa; Mcdermott, Alison M.

Overcoming barriers in Pseudomonas aeruginosa lung infections: engineered nanoparticles for local delivery of a cationic antimicrobial peptide

2015 - COLLOIDS AND SURFACES. B, BIOINTERFACES

D'Angelo, Ivana; Casciaro, Bruno; Miro, Agnese; Quaglia, Fabiana; Mangoni, Maria Luisa; Ungaro, Francesca

Relationship between pulmonary exacerbations and daily physical activity in adults with cystic fibrosis

2015 - BMC PULMONARY MEDICINE

Savi, Daniela; Simmonds, Nicholas; DI PAOLO, Marcello; Quattrucci, Serena; Palange, Paolo; Banya, Winston; Hopkinson, Nicholas S; Bilton, Diana

Relationship between daily physical activity and aerobic fitness in adults with cystic fibrosis

2015 - BMC PULMONARY MEDICINE

SAVI, DANIELA; DI PAOLO, MARCELLO; Simmonds, Nicholas; ONORATI, Paolo; INTERNULLO, MATTIA; QUATTRUCCI, Serena; Winston, Banya; Laveneziana, Pierantonio; PALANGE, Paolo